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focusable> Skip to main content /a> noscript>iframe srchttps://www.googletagmanager.com/ns.html?idGTM-K82H26G height0 width0 styledisplay:none;visibility:hidden>/iframe>/noscript> div classdialog-off-canvas-main-canvas data-off-canvas-main-canvas> div classlayout-container> section classaav-header> div classcontainer> div classrow> div classcol-md-12> nav classnavbar navbar-light navbar-expand-xl> a classnavbar-brand href/ idnavbar-brand-img data-event-categoryHeader data-event-actionClick data-event-labelUnderstandaav Logo> img classlogo__mainlogo src/sites/g/files/brlbcj3716/files/2023-01/UNDERSTANDINGAAV-logo.svg altUnderstandaav Logo /> /a> button classnavbar-toggler typebutton data-togglecollapse data-target#nav aria-controlsnavbarNav aria-expandedfalse aria-labelToggle navigation> span classnavbar-toggler-icon>/span> /button> div classcollapse navbar-collapse idnav> ul classnavbar-nav ml-lg-auto> li classnav-item> a classnav-link text-truncate active href/home data-event-categoryHeader data-event-actionClick data-event-labelHome> Home /a>/li> li classnav-item> a classnav-link text-truncate href/introduction-to-aav data-event-categoryHeader data-event-actionClick data-event-labelIntroduction to AAV> Introduction to AAV /a>/li> li classnav-item> a classnav-link text-truncate href/disease-mechanism data-event-categoryHeader data-event-actionClick data-event-labelDisease mechanism> Disease mechanism /a>/li> li classnav-item> a classnav-link text-truncate href/aav-treatment data-event-categoryHeader data-event-actionClick data-event-labelAAV treatment> AAV treatment /a>/li> li classnav-item> a classnav-link text-truncate href/interactive-tools data-event-categoryHeader data-event-actionClick data-event-labelInteractive tools> Interactive tools /a>/li> /ul> /div> /nav> /div> /div> /div>/section> div classmain> a idmain-content tabindex-1>/a> main rolemain classmain-content> div> div idblock-vifor-understand-aav-content classblock> article data-history-node-id1 about/home typeofschema:WebPage classnode> span propertyschema:name contentHome classhidden>/span> div> div> div> div classbanner banner--bg-image banner-readmore > picture> source srcset/sites/multisite/understandaav/files/2022-11/home_texture_mob.png mediaall and (max-width: 768px) typeimage/jpg alt/> source srcset/sites/multisite/understandaav/files/2022-11/banner-bg.jpg mediaall and (max-width: 1024px) typeimage/png altUnderstanding aav/> source srcset/sites/multisite/understandaav/files/2022-11/banner-bg.jpg mediaall and (min-width: 1366px) typeimage/png altUnderstanding aav/> img classbanner-img src/sites/multisite/understandaav/files/2022-11/banner-bg.jpg altbanner data-path../assets/images/banner/home-banner-expanded.png altUnderstanding aav/> /picture> div classbanner-overlay> div classcontainer> div classrow> div classcol-md-12> div classbanner-content> h1> div>Our understanding of AAV is increasing/div> /h1> p>AAV (ANCA-associated vasculitis) is a group of progressive, rare, and severe autoimmune diseases.sup>1,2/sup>/p> div classreadmore-content> p>AAV (ANCA-associated vasculitis) is a group of progressive, rare, and severe autoimmune diseases.sup>1,2/sup>/p> /div> div classreadmore-content> p>AAV can affect blood vessels in different parts of the body resulting in damage to vital organs such as the lungs, kidneys, nervous system, gastrointestinal system, skin, eyes, and heart.sup>2/sup>/p>p>The three main clinical subtypes of AAV are GPA (granulomatosis with polyangiitis, previously called Wegener’s), MPA (microscopic polyangiitis) and EGPA (eosinophilic granulomatosis with polyangiitis, previously called Churg-Strauss syndrome).sup>3,4/sup> Both GPA and MPA show a lot of clinical commonality, whereas EGPA is distinctly different.sup>5/sup> For this reason, this website will focus mainly on GPA and MPA./p> !-- Button trigger modal --> a href# classcta-link reference data-event-action/home data-event-categoryInternal Link Click data-event-labelReferences & footnotes data-togglemodal data-target#modalpopup471>References & footnotes/a>!-- Modal -->div classtext-modal modal idmodalpopup471 tabindex1 roledialog aria-labelledbymodalLabel aria-hiddentrue> div classmodal-dialog modal-dialog-centered roledocument> div classmodal-content> div classmodal-header> h4 classmodal-title idmodalLabel> References & footnotes /h4> button typebutton classclose data-dismissmodal aria-labelClose> span aria-hiddentrue>img src/sites/multisite/understandaav/themes/vifor_understand_aav/images/template/close.png altclose/>/span> /button> /div> div classmodal-body> p>AAV, ANCA-associated vasculitis; ANCA, anti-neutrophil cytoplasmic antibody; EGPA, eosinophilic granulomatosis with polyangiitis; GPA, granulomatosis with polyangiitis; MPA, microscopic polyangiitis/p>ol>li>Hutton HL, et al. em>Semin Nephrol/em> 2017;37(5):418–35./li>li>Al-Hussain T, et al. em>Adv Anat Pathol/em> 2017;24(4):226–34./li>li>Jennette JC, et al. em>Arthritis Rheum/em> 2013;65(1):1–11./li>li>Yates M, Watts R. em>Clin Med/em> (Lond) 2017;17(1):60–4./li>li>Pagnoux C. em>Eur J Rheumatol /em>2016;3(3):122–33./li>/ol> /div> /div> /div>/div>/div>a href# classreadmore-btn data-event-categoryInternal Link Click data-event-action/home data-event-labelRead more>Read more/a> /div> /div> /div> /div> /div>/div>/div> div>div classblurb blurb--clinical-data text-img > div classcontainer idsec481> div classrow> div classcol-md-6> div classtext-img-content> h3> Discover the key clinical data in AAV /h3> p>Our current understanding of patient outcomes in ANCA-associated vasculitis (AAV) is rapidly evolving as more studies are being conducted./p>p>Click here to read the key clinical research papers to find out more about treatment outcomes in AAV./p> a href/aav-treatment#sec981 classcta click-here data-event-categoryInternal Link Click data-event-action/home data-event-labelClick here>Click here/a> /div> /div> div classcol-md-6> div classimage-wraper> picture> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key-mob.png altdiscover-the-key mediaall and (max-width: 480px) typeimage/jpeg/> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key mediaall and (max-width: 768px) typeimage/jpeg/> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key mediaall and (max-width: 1366px) typeimage/jpeg/> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key mediaall and (min-width: 1367px) typeimage/jpeg/> img src/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key/> /picture> /div> /div> /div> /div>/div>/div> div>section> div classcontainer> div classrow> div classcol-md-12> div classsignpost-block-main> div classsign-post-cards sign-post-video> div classcontainer-fluid> div classrow> div classcol-md-6> div classcards-vertical cards-vertical--card-vertical-video reference> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> iframe srchttps://players.brightcove.net/5987230675001/default_default/index.html?videoId6361192304112 frameborder0 allowautoplay; fullscreen; picture-in-picture allowfullscreen titleanemia.mov>/iframe> /div> div classvertical-card-content> h4>AAV mechanism of disease/h4> p>See how the interaction between neutrophils and the alternative complement system are at the heart of the vasculitis process in AAV./p> a classcta href/disease-mechanism data-event-categoryInternal Link Click data-event-action/home data-event-labelAAV mechanism of disease>More information/a> /div> /div> /div> /div> /div> div classcol-md-6> div classcards-vertical cards-vertical-- down-arrow> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href data-event-categoryInternal Link Click data-event-action/home data-event-label> picture> source altEular srcset/sites/multisite/understandaav/files/2023-05/infographic_0.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> source altEular srcset/sites/multisite/understandaav/files/2023-05/infographic_0.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> source altEular srcset/sites/multisite/understandaav/files/2023-05/infographic_0.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> img src/sites/multisite/understandaav/files/2023-05/infographic_0.png altEular data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> /picture> /a> /div> div classvertical-card-content> h4>EULAR 2022 recommendations/h4> p>Download our infographic to view the latest updates and recommendations from EULAR around the treatment of AAV./p> a classcta href/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf target_blank data-event-categoryDownload data-event-action/home data-event-labelDownload>Download/a> /div> /div> /div> /div> /div> /div> /div> /div> div classsign-post-cards full-column> div classcontainer-fluid> div classrow> div classcol-md-12> div classcards-vertical cards-vertical-- reference> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> /a> /div> div classvertical-card-content> h4>Helpful resources/h4> p>Use our interactive educational tools to discover more about ANCA-associated vasculitis (AAV)./p>p>AAV World is an educational game that sheds light on the clinical priorities in AAV in a fun and interactive way. Take part in AAV World and test your skills through a mix of challenges, brainteasers, riddles and quizzes. Or why not join the Rare Disease Investigation Team and put your expertise to the test in our mysterious challenge./p> a classcta href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-labelHelpful resources>Complete the challenges/a> /div> /div> /div> /div> /div> div classcol-md-6> div classcards-vertical cards-vertical--> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> picture> source altERA2022 srcset/sites/multisite/understandaav/files/2022-11/card1.jpg mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altERA2022 srcset/sites/multisite/understandaav/files/2022-11/card1.jpg mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altERA2022 srcset/sites/multisite/understandaav/files/2022-11/card1.jpg mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> img src/sites/multisite/understandaav/files/2022-11/card1.jpg altERA2022 data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> /picture> /a> /div> /div> /div> /div> /div> div classcol-md-6> div classcards-vertical cards-vertical--> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href/ data-event-categoryInternal Link Click data-event-action/home data-event-label/> picture> source altHelpful resources srcset/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/> source altHelpful resources srcset/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/> source altHelpful resources srcset/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/> img src/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png altHelpful resources data-event-categoryInternal Link Click data-event-action/home data-event-label/> /picture> /a> /div> /div> /div> /div> /div> /div> /div> div classcontainer-fluid> div classrow> div classcol-md-12> div classback-top-wrap> a href# classcta back-to-top data-event-categoryInternal Link Click data-event-action/home data-event-labelBack to top>Back to top/a> /div> /div> /div> /div> /div> /div> /div> /div> /div>/section>/div> div> div classcontent-wrapper content-doc idsec551> div classcontainer> div classrow> div classcol-md-12> div classtext-long>div classtext-long>div>a hrefhttps://www.myancavasculitis.com/ target_blank data-event-action/ch-en/home data-event-categoryExternal Link Click data-event-labelSee me hear me>img classvisible-desktop src/sites/g/files/brlbcj3716/files/2023-01/banner-desktop_English.png altsee me hear me data-event-action/ch-en/home data-event-categoryExternal Link Click data-event-labelSee me hear me>img classvisible-mobile src/sites/g/files/brlbcj3716/files/2023-01/banner-mobile_English.png altsee me hear me data-event-action/ch-en/home data-event-categoryExternal Link Click data-event-labelSee me hear me>/a>/div>/div>/div> /div> /div> /div> /div> /div> div> div classsign-post-cards> div classcontainer> div classrow> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altintroduction-to-AAV srcset/sites/multisite/understandaav/files/2022-11/introduction-to-AAV-mob.jpg mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/introduction-to-aav> source altIntroduction to AAV srcset/sites/multisite/understandaav/files/2022-11/introduction-to-AAV-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/introduction-to-aav> source altIntroduction to AAV srcset/sites/multisite/understandaav/files/2022-11/introduction-to-AAV-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/introduction-to-aav> img src/sites/multisite/understandaav/files/2022-11/introduction-to-AAV-card-img%402x.png altIntroduction to AAV data-event-categoryInternal Link Click data-event-action/home data-event-label/introduction-to-aav> /picture> /div> div classvertical-card-content> h4>Introduction to AAV/h4> p>AAV is a rare, severe small vessel vasculitis that affects multiple organs and has a high acute mortality risksup>1/sup>/p> a classcta href/introduction-to-aav data-event-categoryInternal Link Click data-event-action/home data-event-labelIntroduction to AAV>Read more/a> /div> /div> /div> /div> /div> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altDisease Mechanism srcset/sites/multisite/understandaav/files/2022-12/disease-mechanism-card-img.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> source altDisease Mechanism srcset/sites/multisite/understandaav/files/2022-11/disease-mechanism-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> source altDisease Mechanism srcset/sites/multisite/understandaav/files/2022-11/disease-mechanism-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> img src/sites/multisite/understandaav/files/2022-11/disease-mechanism-card-img%402x.png altDisease Mechanism data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> /picture> /div> div classvertical-card-content> h4>Disease Mechanism/h4> p>The interaction between the activated alternative complement pathway, neutrophils and C5a is at the heart of vasculitic damage in AAVsup>2/sup>/p> a classcta href/disease-mechanism data-event-categoryInternal Link Click data-event-action/home data-event-labelDisease Mechanism>Read more/a> /div> /div> /div> /div> /div> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altAAV treatment srcset/sites/multisite/understandaav/files/2022-12/AAV-treatment-card-img.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> source altAAV treatment srcset/sites/multisite/understandaav/files/2022-11/AAV-treatment-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> source altAAV treatment srcset/sites/multisite/understandaav/files/2022-11/AAV-treatment-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> img src/sites/multisite/understandaav/files/2022-11/AAV-treatment-card-img%402x.png altAAV treatment data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> /picture> /div> div classvertical-card-content> h4>AAV treatment/h4> p>A framework of practice for the treatment and management of AAV patients/p> a classcta href/aav-treatment data-event-categoryInternal Link Click data-event-action/home data-event-labelAAV treatment>Read more/a> /div> /div> /div> /div> /div> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altInteractive tools srcset/sites/multisite/understandaav/files/2022-12/interactive-tools-card-img.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altInteractive tools srcset/sites/multisite/understandaav/files/2022-11/interactive-tools-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altInteractive tools srcset/sites/multisite/understandaav/files/2022-11/interactive-tools-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> img src/sites/multisite/understandaav/files/2022-11/interactive-tools-card-img%402x.png altInteractive tools data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> /picture> /div> div classvertical-card-content> h4>Interactive tools/h4> p>Use our interactive educational tools to discover more about AAV/p> a classcta href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-labelInteractive tools>Read more/a> /div> /div> /div> /div> /div> /div> /div> div classcontainer> div classrow> div classcol-md-12> !-- Button trigger modal --> a href# classcta-link reference data-event-action/home data-event-categoryInternal Link Click data-event-labelReferences & footnotes data-togglemodal data-target#modalpopup501>References & footnotes/a>!-- Modal -->div classtext-modal modal idmodalpopup501 tabindex1 roledialog aria-labelledbymodalLabel aria-hiddentrue> div classmodal-dialog modal-dialog-centered roledocument> div classmodal-content> div classmodal-header> h4 classmodal-title idmodalLabel> References & footnotes /h4> button typebutton classclose data-dismissmodal aria-labelClose> span aria-hiddentrue>img src/sites/multisite/understandaav/themes/vifor_understand_aav/images/template/close.png altclose/>/span> /button> /div> div classmodal-body> p>AAV, ANCA-associated vasculitis; ANCA, anti-neutrophil cytoplasmic antibody;br>C5a, complement 5a./p>ol> li>Hutton HL, et al. em>Semin Nephrol/em> 2017;37(5):418–35./li> li>Bekker P, et al. em>PLoS One/em> 2016;11(10):e0164646./li>/ol> /div> /div> /div>/div> /div> /div> /div>/div>/div> /div> /div>/article> /div> div classmodal home-modal fade splashmodal idMymodal1 tabindex-1 data-backdropstatic 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option value/nordics classtest data-doccheck data-swissrx data-thumbnailhttps://www.understandaav.com/sites/multisite/understandaav/files/2023-01/sweden-min.png> Sweden /option> option value/ch-en classtest data-doccheck data-swissrx data-thumbnailhttps://www.understandaav.com/sites/multisite/understandaav/files/2022-11/switzerland-min.png> Switzerland /option> /select> div classcountry-select> button classbtn-select value>/button> div classcountry-selection> ul classcountries>/ul> /div> /div> /div> /div> div classmodal-footer> a typebutton classcta-link cta-link-primary>Back to options/a> div classbutton-wrapper> a hrefjavascript:void(0); typebutton classcta-link doccheck-continue cta-link-secondary>Continue/a> /div> /div> /div> /div>/div> div classmodal home-modal fade splashmodal available idMymodal3 tabindex-1 data-backdropstatic data-keyboardfalse roledialog aria-labelledbyMymodal3 aria-hiddentrue> div classmodal-dialog modal-dialog-centered roledocument> div classmodal-content> div classmodal-header> h5 classmodal-title idexampleModalLongTitle>Available Soon/h5> /div> div classmodal-body wraper-body> div classbox-wrap> p classtext-center> The website is currently being updated and will be made available soon./p> /div> /div> div classmodal-footer> a typebutton classctabutton continue data-dismissmodal>Close/a> /div> /div> /div>/div>div idblock-idicefooterupper classblock> div> div> div classaccordion-wrapper secondary> div classcontainer> div classrow> div classcol-md-12> div idaccordion-three> div classcard> div classcard-header idheading-3> h4 classcollapsed data-togglecollapse data-target#accordion-collapse-3 aria-expandedfalse aria-controlsaccordion-collapse-3 data-event-categoryInternal Link Click data-event-action/home data-event-labelAdditional Resources> span classaccordion-text data-event-categoryInternal Link Click data-event-action/home data-event-labelAdditional Resources>Additional Resources/span> span classaccordion-arrow data-event-categoryInternal Link Click data-event-action/home data-event-labelAdditional Resources>/span> /h4> /div> div idaccordion-collapse-3 classcollapse aria-labelledbyheading-3 data-parent#accordion-three> div classcard-body> div classtext-stack-wrapper image-block> div classcontainer> div classrow> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EUVAS/h5> p>European Vasculitis Society website/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://vasculitis.org/ hrefhttps://vasculitis.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>ASN/h5> p>American Society of Nephrology/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.asn-online.org/ hrefhttps://www.asn-online.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>ACR/h5> p>American College of Rheumatology/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.rheumatology.org/ hrefhttps://www.rheumatology.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>ERA/h5> p>European Renal Association/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.era-online.org/en/ hrefhttps://www.era-online.org/en/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EULAR/h5> p>European Alliance of Associations for Rheumatology/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.eular.org/index.cfm hrefhttps://www.eular.org/index.cfm>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>KDIGO/h5> p>Kidney Disease Improving Global Outcomes/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://kdigo.org/ hrefhttps://kdigo.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>KDIGO recommendations/h5> p>KDIGO recommendations for the management of individuals with glomerular diseases/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://kdigo.org/guidelines/gd/ hrefhttps://kdigo.org/guidelines/gd/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EULAR treatment recommendations/h5> p>EULAR recommendations for the management of ANCA-associated vasculitis/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://ard.bmj.com/content/early/2023/03/16/ard-2022-223764 hrefhttps://ard.bmj.com/content/early/2023/03/16/ard-2022-223764>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EULAR recommendations pocket guide/h5> p>Summary of EULAR recommendations for the management of GPA/MPA/p> a classcta down-arrow target_blank href/sites/multisite/understandaav/files/2023-05/Pocket%20guide%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf>Download/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>Patient videos and quality of life/h5> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.myancavasculitis.com/ hrefhttps://www.myancavasculitis.com/>Read more/a> /div> /div>/div> /div> /div>/div> /div> /div> /div> /div> /div> div classcol-md-12> div idaccordion-four> div classcard> div classcard-header idheading-4> h4 classcollapsed data-togglecollapse data-target#accordion-collapse-4 aria-expandedfalse aria-controlsaccordion-collapse-4 data-event-categoryInternal Link Click data-event-action/home data-event-labelPatient Support Organisations> span classaccordion-text data-event-categoryInternal Link Click data-event-action/home data-event-labelPatient Support Organisations>Patient Support Organisations/span> span classaccordion-arrow data-event-categoryInternal Link Click data-event-action/home data-event-labelPatient Support Organisations>/span> /h4> /div> div idaccordion-collapse-4 classcollapse aria-labelledbyheading-4 data-parent#accordion-four> div classcard-body> div classtext-stack-wrapper image-block> div classcontainer> div classrow> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon1.svg/> /div> div classcontent-block> h5>Vasculitis International/h5> p>Europe/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.vasculitisint.com/ hrefhttps://www.vasculitisint.com/>www.vasculitis.eu/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon2.svg/> /div> div classcontent-block> h5>Selbsthilfe Vaskulitis e.V./h5> p>Germany/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.vasculitisint.com/vpag/vaskulitis-e-v/ hrefhttps://www.vasculitisint.com/vpag/vaskulitis-e-v/>www.vaskulitisverein-rlp.de/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon3.svg/> /div> div classcontent-block> h5>Associazione Pazienti della Sindrome di Churg Strauss/h5> p>Italy/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://apacs-egpa.org/ hrefhttps://apacs-egpa.org/>www.apacs-egpa.org/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon4.svg/> /div> div classcontent-block> h5>Suomen Vaskuliittiyhdistys ry/h5> p>Finland/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.vaskuliittiyhdistys.fi/ hrefhttps://www.vaskuliittiyhdistys.fi/>www.vaskuliittiyhdistys.fi/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon5.svg/> /div> div classcontent-block> h5>Selbsthilfe Vaskulitis Mainz/h5> p>Germany/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttp:// vaskulitis-mainz@gmx.de/ hrefhttp:// vaskulitis-mainz@gmx.de/>vaskulitis-mainz@gmx.de/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon6.svg/> /div> div classcontent-block> h5>Vasculitis Stichting/h5> p>Netherlands/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://vasculitis.nl/ hrefhttps://vasculitis.nl/>www.vasculitis.nl/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon7.svg/> /div> div classcontent-block> h5>Liga Portuguesa Contra as Doencas Reumaticas/h5> p>Portugal/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.lpcdr.org.pt/ hrefhttps://www.lpcdr.org.pt/>www.lpcdr.org.pt/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon8.svg/> /div> div classcontent-block> h5>Association Vascularites/h5> p>France/Belgium/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.association-vascularites.org/ hrefhttps://www.association-vascularites.org/>www.association-vascularites.org/a> /div> /div>/div> div classd-none> div classstack-content main-block> div classcontent-block> p>Ireland/p> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon10.svg/> /div> div classcontent-block> h5>Asociación Española de Vasculitis Sistémicas/h5> p>Spain/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttp://www.vasculitis.es/ hrefhttp://www.vasculitis.es/>www.sid-inico.usal.es/a> /div> /div>/div> div 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hrefhttps://www.anmar-italia.it/>www.anmar-italia.it/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/ANZ-Logo-rev.png/> /div> div classcontent-block> h5>Australia and New Zealand Vasculitis Society/h5> p>Australia / New Zealand/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.anzvasculitis.org/ hrefhttps://www.anzvasculitis.org/>www.anzvasculitis.org/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/Logo-FEDER-858x350.png/> /div> div classcontent-block> h5>Federación Española de Enfermedades Raras/h5> p>Spain/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.enfermedades-raras.org/ 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data-event-categoryHeader data-event-actionClick data-event-labelHome> Home /a>/li> li classnav-item> a classnav-link text-truncate href/introduction-to-aav data-event-categoryHeader data-event-actionClick data-event-labelIntroduction to AAV> Introduction to AAV /a>/li> li classnav-item> a classnav-link text-truncate href/disease-mechanism data-event-categoryHeader data-event-actionClick data-event-labelDisease mechanism> Disease mechanism /a>/li> li classnav-item> a classnav-link text-truncate href/aav-treatment data-event-categoryHeader data-event-actionClick data-event-labelAAV treatment> AAV treatment /a>/li> li classnav-item> a classnav-link text-truncate href/interactive-tools data-event-categoryHeader data-event-actionClick data-event-labelInteractive tools> Interactive tools /a>/li> /ul> /div> /nav> /div> /div> /div>/section> div classmain> a idmain-content tabindex-1>/a> main rolemain classmain-content> div> div idblock-vifor-understand-aav-content classblock> article data-history-node-id1 about/home typeofschema:WebPage classnode> span propertyschema:name contentHome classhidden>/span> div> div> div> div classbanner banner--bg-image banner-readmore > picture> source srcset/sites/multisite/understandaav/files/2022-11/home_texture_mob.png mediaall and (max-width: 768px) typeimage/jpg alt/> source srcset/sites/multisite/understandaav/files/2022-11/banner-bg.jpg mediaall and (max-width: 1024px) typeimage/png altUnderstanding aav/> source srcset/sites/multisite/understandaav/files/2022-11/banner-bg.jpg mediaall and (min-width: 1366px) typeimage/png altUnderstanding aav/> img classbanner-img src/sites/multisite/understandaav/files/2022-11/banner-bg.jpg altbanner data-path../assets/images/banner/home-banner-expanded.png altUnderstanding aav/> /picture> div classbanner-overlay> div classcontainer> div classrow> div classcol-md-12> div classbanner-content> h1> div>Our understanding of AAV is increasing/div> /h1> p>AAV (ANCA-associated vasculitis) is a group of progressive, rare, and severe autoimmune diseases.sup>1,2/sup>/p> div classreadmore-content> p>AAV (ANCA-associated vasculitis) is a group of progressive, rare, and severe autoimmune diseases.sup>1,2/sup>/p> /div> div classreadmore-content> p>AAV can affect blood vessels in different parts of the body resulting in damage to vital organs such as the lungs, kidneys, nervous system, gastrointestinal system, skin, eyes, and heart.sup>2/sup>/p>p>The three main clinical subtypes of AAV are GPA (granulomatosis with polyangiitis, previously called Wegener’s), MPA (microscopic polyangiitis) and EGPA (eosinophilic granulomatosis with polyangiitis, previously called Churg-Strauss syndrome).sup>3,4/sup> Both GPA and MPA show a lot of clinical commonality, whereas EGPA is distinctly different.sup>5/sup> For this reason, this website will focus mainly on GPA and MPA./p> !-- Button trigger modal --> a href# classcta-link reference data-event-action/home data-event-categoryInternal Link Click data-event-labelReferences & footnotes data-togglemodal data-target#modalpopup471>References & footnotes/a>!-- Modal -->div classtext-modal modal idmodalpopup471 tabindex1 roledialog aria-labelledbymodalLabel aria-hiddentrue> div classmodal-dialog modal-dialog-centered roledocument> div classmodal-content> div classmodal-header> h4 classmodal-title idmodalLabel> References & footnotes /h4> button typebutton classclose data-dismissmodal aria-labelClose> span aria-hiddentrue>img src/sites/multisite/understandaav/themes/vifor_understand_aav/images/template/close.png altclose/>/span> /button> /div> div classmodal-body> p>AAV, ANCA-associated vasculitis; ANCA, anti-neutrophil cytoplasmic antibody; EGPA, eosinophilic granulomatosis with polyangiitis; GPA, granulomatosis with polyangiitis; MPA, microscopic polyangiitis/p>ol>li>Hutton HL, et al. em>Semin Nephrol/em> 2017;37(5):418–35./li>li>Al-Hussain T, et al. em>Adv Anat Pathol/em> 2017;24(4):226–34./li>li>Jennette JC, et al. em>Arthritis Rheum/em> 2013;65(1):1–11./li>li>Yates M, Watts R. em>Clin Med/em> (Lond) 2017;17(1):60–4./li>li>Pagnoux C. em>Eur J Rheumatol /em>2016;3(3):122–33./li>/ol> /div> /div> /div>/div>/div>a href# classreadmore-btn data-event-categoryInternal Link Click data-event-action/home data-event-labelRead more>Read more/a> /div> /div> /div> /div> /div>/div>/div> div>div classblurb blurb--clinical-data text-img > div classcontainer idsec481> div classrow> div classcol-md-6> div classtext-img-content> h3> Discover the key clinical data in AAV /h3> p>Our current understanding of patient outcomes in ANCA-associated vasculitis (AAV) is rapidly evolving as more studies are being conducted./p>p>Click here to read the key clinical research papers to find out more about treatment outcomes in AAV./p> a href/aav-treatment#sec981 classcta click-here data-event-categoryInternal Link Click data-event-action/home data-event-labelClick here>Click here/a> /div> /div> div classcol-md-6> div classimage-wraper> picture> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key-mob.png altdiscover-the-key mediaall and (max-width: 480px) typeimage/jpeg/> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key mediaall and (max-width: 768px) typeimage/jpeg/> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key mediaall and (max-width: 1366px) typeimage/jpeg/> source srcset/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key mediaall and (min-width: 1367px) typeimage/jpeg/> img src/sites/multisite/understandaav/files/2022-11/discover-the-key.png altdiscover-the-key/> /picture> /div> /div> /div> /div>/div>/div> div>section> div classcontainer> div classrow> div classcol-md-12> div classsignpost-block-main> div classsign-post-cards sign-post-video> div classcontainer-fluid> div classrow> div classcol-md-6> div classcards-vertical cards-vertical--card-vertical-video reference> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> iframe srchttps://players.brightcove.net/5987230675001/default_default/index.html?videoId6361192304112 frameborder0 allowautoplay; fullscreen; picture-in-picture allowfullscreen titleanemia.mov>/iframe> /div> div classvertical-card-content> h4>AAV mechanism of disease/h4> p>See how the interaction between neutrophils and the alternative complement system are at the heart of the vasculitis process in AAV./p> a classcta href/disease-mechanism data-event-categoryInternal Link Click data-event-action/home data-event-labelAAV mechanism of disease>More information/a> /div> /div> /div> /div> /div> div classcol-md-6> div classcards-vertical cards-vertical-- down-arrow> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href data-event-categoryInternal Link Click data-event-action/home data-event-label> picture> source altEular srcset/sites/multisite/understandaav/files/2023-05/infographic_0.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> source altEular srcset/sites/multisite/understandaav/files/2023-05/infographic_0.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> source altEular srcset/sites/multisite/understandaav/files/2023-05/infographic_0.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> img src/sites/multisite/understandaav/files/2023-05/infographic_0.png altEular data-event-categoryInternal Link Click data-event-action/home data-event-label/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf> /picture> /a> /div> div classvertical-card-content> h4>EULAR 2022 recommendations/h4> p>Download our infographic to view the latest updates and recommendations from EULAR around the treatment of AAV./p> a classcta href/sites/multisite/understandaav/files/2023-05/Infographic%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf target_blank data-event-categoryDownload data-event-action/home data-event-labelDownload>Download/a> /div> /div> /div> /div> /div> /div> /div> /div> div classsign-post-cards full-column> div classcontainer-fluid> div classrow> div classcol-md-12> div classcards-vertical cards-vertical-- reference> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> /a> /div> div classvertical-card-content> h4>Helpful resources/h4> p>Use our interactive educational tools to discover more about ANCA-associated vasculitis (AAV)./p>p>AAV World is an educational game that sheds light on the clinical priorities in AAV in a fun and interactive way. Take part in AAV World and test your skills through a mix of challenges, brainteasers, riddles and quizzes. Or why not join the Rare Disease Investigation Team and put your expertise to the test in our mysterious challenge./p> a classcta href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-labelHelpful resources>Complete the challenges/a> /div> /div> /div> /div> /div> div classcol-md-6> div classcards-vertical cards-vertical--> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> picture> source altERA2022 srcset/sites/multisite/understandaav/files/2022-11/card1.jpg mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altERA2022 srcset/sites/multisite/understandaav/files/2022-11/card1.jpg mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altERA2022 srcset/sites/multisite/understandaav/files/2022-11/card1.jpg mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> img src/sites/multisite/understandaav/files/2022-11/card1.jpg altERA2022 data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> /picture> /a> /div> /div> /div> /div> /div> div classcol-md-6> div classcards-vertical cards-vertical--> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> a href/ data-event-categoryInternal Link Click data-event-action/home data-event-label/> picture> source altHelpful resources srcset/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/> source altHelpful resources srcset/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/> source altHelpful resources srcset/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/> img src/sites/multisite/understandaav/files/2022-11/challenge-2%5B1%5D%402x.png altHelpful resources data-event-categoryInternal Link Click data-event-action/home data-event-label/> /picture> /a> /div> /div> /div> /div> /div> /div> /div> div classcontainer-fluid> div classrow> div classcol-md-12> div classback-top-wrap> a href# classcta back-to-top data-event-categoryInternal Link Click data-event-action/home data-event-labelBack to top>Back to top/a> /div> /div> /div> /div> /div> /div> /div> /div> /div>/section>/div> div> div classcontent-wrapper content-doc idsec551> div classcontainer> div classrow> div classcol-md-12> div classtext-long>div classtext-long>div>a hrefhttps://www.myancavasculitis.com/ target_blank data-event-action/ch-en/home data-event-categoryExternal Link Click data-event-labelSee me hear me>img classvisible-desktop src/sites/g/files/brlbcj3716/files/2023-01/banner-desktop_English.png altsee me hear me data-event-action/ch-en/home data-event-categoryExternal Link Click data-event-labelSee me hear me>img classvisible-mobile src/sites/g/files/brlbcj3716/files/2023-01/banner-mobile_English.png altsee me hear me data-event-action/ch-en/home data-event-categoryExternal Link Click data-event-labelSee me hear me>/a>/div>/div>/div> /div> /div> /div> /div> /div> div> div classsign-post-cards> div classcontainer> div classrow> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altintroduction-to-AAV 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classvertical-card-content> h4>Introduction to AAV/h4> p>AAV is a rare, severe small vessel vasculitis that affects multiple organs and has a high acute mortality risksup>1/sup>/p> a classcta href/introduction-to-aav data-event-categoryInternal Link Click data-event-action/home data-event-labelIntroduction to AAV>Read more/a> /div> /div> /div> /div> /div> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altDisease Mechanism srcset/sites/multisite/understandaav/files/2022-12/disease-mechanism-card-img.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> source altDisease Mechanism srcset/sites/multisite/understandaav/files/2022-11/disease-mechanism-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> source altDisease Mechanism srcset/sites/multisite/understandaav/files/2022-11/disease-mechanism-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> img src/sites/multisite/understandaav/files/2022-11/disease-mechanism-card-img%402x.png altDisease Mechanism data-event-categoryInternal Link Click data-event-action/home data-event-label/disease-mechanism> /picture> /div> div classvertical-card-content> h4>Disease Mechanism/h4> p>The interaction between the activated alternative complement pathway, neutrophils and C5a is at the heart of vasculitic damage in AAVsup>2/sup>/p> a classcta href/disease-mechanism data-event-categoryInternal Link Click data-event-action/home data-event-labelDisease Mechanism>Read more/a> /div> /div> /div> /div> /div> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altAAV treatment srcset/sites/multisite/understandaav/files/2022-12/AAV-treatment-card-img.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> source altAAV treatment srcset/sites/multisite/understandaav/files/2022-11/AAV-treatment-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> source altAAV treatment srcset/sites/multisite/understandaav/files/2022-11/AAV-treatment-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> img src/sites/multisite/understandaav/files/2022-11/AAV-treatment-card-img%402x.png altAAV treatment data-event-categoryInternal Link Click data-event-action/home data-event-label/aav-treatment> /picture> /div> div classvertical-card-content> h4>AAV treatment/h4> p>A framework of practice for the treatment and management of AAV patients/p> a classcta href/aav-treatment data-event-categoryInternal Link Click data-event-action/home data-event-labelAAV treatment>Read more/a> /div> /div> /div> /div> /div> div classcol-md-4> div classcards-vertical cards-vertical-- pink> div classcard-vertical-main> div classcard-vertical-list> div classvertical-card-image> picture> source altInteractive tools srcset/sites/multisite/understandaav/files/2022-12/interactive-tools-card-img.png mediaall and (max-width: 480px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altInteractive tools srcset/sites/multisite/understandaav/files/2022-11/interactive-tools-card-img%402x.png mediaall and (max-width: 1366px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> source altInteractive tools srcset/sites/multisite/understandaav/files/2022-11/interactive-tools-card-img%402x.png mediaall and (min-width: 1367px) typeimage/jpg data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> img src/sites/multisite/understandaav/files/2022-11/interactive-tools-card-img%402x.png altInteractive tools data-event-categoryInternal Link Click data-event-action/home data-event-label/interactive-tools> /picture> /div> div classvertical-card-content> h4>Interactive tools/h4> p>Use our interactive educational tools to discover more about AAV/p> a classcta href/interactive-tools data-event-categoryInternal Link Click data-event-action/home data-event-labelInteractive tools>Read more/a> /div> /div> /div> /div> /div> /div> /div> div classcontainer> div classrow> div classcol-md-12> !-- Button trigger modal --> a href# classcta-link reference data-event-action/home data-event-categoryInternal Link Click data-event-labelReferences & footnotes data-togglemodal data-target#modalpopup501>References & footnotes/a>!-- Modal -->div classtext-modal modal idmodalpopup501 tabindex1 roledialog aria-labelledbymodalLabel aria-hiddentrue> div classmodal-dialog modal-dialog-centered roledocument> div classmodal-content> div classmodal-header> h4 classmodal-title idmodalLabel> References & footnotes /h4> button typebutton classclose data-dismissmodal aria-labelClose> span aria-hiddentrue>img src/sites/multisite/understandaav/themes/vifor_understand_aav/images/template/close.png altclose/>/span> /button> /div> div classmodal-body> p>AAV, ANCA-associated vasculitis; ANCA, anti-neutrophil cytoplasmic antibody;br>C5a, complement 5a./p>ol> li>Hutton HL, et al. em>Semin Nephrol/em> 2017;37(5):418–35./li> li>Bekker P, et al. em>PLoS One/em> 2016;11(10):e0164646./li>/ol> /div> /div> /div>/div> /div> /div> /div>/div>/div> /div> /div>/article> /div> div classmodal home-modal fade splashmodal idMymodal1 tabindex-1 data-backdropstatic 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option value/nordics classtest data-doccheck data-swissrx data-thumbnailhttps://www.understandaav.com/sites/multisite/understandaav/files/2023-01/sweden-min.png> Sweden /option> option value/ch-en classtest data-doccheck data-swissrx data-thumbnailhttps://www.understandaav.com/sites/multisite/understandaav/files/2022-11/switzerland-min.png> Switzerland /option> /select> div classcountry-select> button classbtn-select value>/button> div classcountry-selection> ul classcountries>/ul> /div> /div> /div> /div> div classmodal-footer> a typebutton classcta-link cta-link-primary>Back to options/a> div classbutton-wrapper> a hrefjavascript:void(0); typebutton classcta-link doccheck-continue cta-link-secondary>Continue/a> /div> /div> /div> /div>/div> div classmodal home-modal fade splashmodal available idMymodal3 tabindex-1 data-backdropstatic data-keyboardfalse roledialog aria-labelledbyMymodal3 aria-hiddentrue> div classmodal-dialog modal-dialog-centered roledocument> div classmodal-content> div classmodal-header> h5 classmodal-title idexampleModalLongTitle>Available Soon/h5> /div> div classmodal-body wraper-body> div classbox-wrap> p classtext-center> The website is currently being updated and will be made available soon./p> /div> /div> div classmodal-footer> a typebutton classctabutton continue data-dismissmodal>Close/a> /div> /div> /div>/div>div idblock-idicefooterupper classblock> div> div> div classaccordion-wrapper secondary> div classcontainer> div classrow> div classcol-md-12> div idaccordion-three> div classcard> div classcard-header idheading-3> h4 classcollapsed data-togglecollapse data-target#accordion-collapse-3 aria-expandedfalse aria-controlsaccordion-collapse-3 data-event-categoryInternal Link Click data-event-action/home data-event-labelAdditional Resources> span classaccordion-text data-event-categoryInternal Link Click data-event-action/home data-event-labelAdditional Resources>Additional Resources/span> span classaccordion-arrow data-event-categoryInternal Link Click data-event-action/home data-event-labelAdditional Resources>/span> /h4> /div> div idaccordion-collapse-3 classcollapse aria-labelledbyheading-3 data-parent#accordion-three> div classcard-body> div classtext-stack-wrapper image-block> div classcontainer> div classrow> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EUVAS/h5> p>European Vasculitis Society website/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://vasculitis.org/ hrefhttps://vasculitis.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>ASN/h5> p>American Society of Nephrology/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.asn-online.org/ hrefhttps://www.asn-online.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>ACR/h5> p>American College of Rheumatology/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.rheumatology.org/ hrefhttps://www.rheumatology.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>ERA/h5> p>European Renal Association/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.era-online.org/en/ hrefhttps://www.era-online.org/en/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EULAR/h5> p>European Alliance of Associations for Rheumatology/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.eular.org/index.cfm hrefhttps://www.eular.org/index.cfm>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>KDIGO/h5> p>Kidney Disease Improving Global Outcomes/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://kdigo.org/ hrefhttps://kdigo.org/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>KDIGO recommendations/h5> p>KDIGO recommendations for the management of individuals with glomerular diseases/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://kdigo.org/guidelines/gd/ hrefhttps://kdigo.org/guidelines/gd/>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EULAR treatment recommendations/h5> p>EULAR recommendations for the management of ANCA-associated vasculitis/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://ard.bmj.com/content/early/2023/03/16/ard-2022-223764 hrefhttps://ard.bmj.com/content/early/2023/03/16/ard-2022-223764>Read more/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>EULAR recommendations pocket guide/h5> p>Summary of EULAR recommendations for the management of GPA/MPA/p> a classcta down-arrow target_blank href/sites/multisite/understandaav/files/2023-05/Pocket%20guide%20-%20EULAR%202022%20recommendations%20for%20managing%20AAV.pdf>Download/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classcontent-block> h5>Patient videos and quality of life/h5> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.myancavasculitis.com/ hrefhttps://www.myancavasculitis.com/>Read more/a> /div> /div>/div> /div> /div>/div> /div> /div> /div> /div> /div> div classcol-md-12> div idaccordion-four> div classcard> div classcard-header idheading-4> h4 classcollapsed data-togglecollapse data-target#accordion-collapse-4 aria-expandedfalse aria-controlsaccordion-collapse-4 data-event-categoryInternal Link Click data-event-action/home data-event-labelPatient Support Organisations> span classaccordion-text data-event-categoryInternal Link Click data-event-action/home data-event-labelPatient Support Organisations>Patient Support Organisations/span> span classaccordion-arrow data-event-categoryInternal Link Click data-event-action/home data-event-labelPatient Support Organisations>/span> /h4> /div> div idaccordion-collapse-4 classcollapse aria-labelledbyheading-4 data-parent#accordion-four> div classcard-body> div classtext-stack-wrapper image-block> div classcontainer> div classrow> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon1.svg/> /div> div classcontent-block> h5>Vasculitis International/h5> p>Europe/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.vasculitisint.com/ hrefhttps://www.vasculitisint.com/>www.vasculitis.eu/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon2.svg/> /div> div classcontent-block> h5>Selbsthilfe Vaskulitis e.V./h5> p>Germany/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.vasculitisint.com/vpag/vaskulitis-e-v/ hrefhttps://www.vasculitisint.com/vpag/vaskulitis-e-v/>www.vaskulitisverein-rlp.de/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon3.svg/> /div> div classcontent-block> h5>Associazione Pazienti della Sindrome di Churg Strauss/h5> p>Italy/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://apacs-egpa.org/ hrefhttps://apacs-egpa.org/>www.apacs-egpa.org/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon4.svg/> /div> div classcontent-block> h5>Suomen Vaskuliittiyhdistys ry/h5> p>Finland/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.vaskuliittiyhdistys.fi/ hrefhttps://www.vaskuliittiyhdistys.fi/>www.vaskuliittiyhdistys.fi/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon5.svg/> /div> div classcontent-block> h5>Selbsthilfe Vaskulitis Mainz/h5> p>Germany/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttp:// vaskulitis-mainz@gmx.de/ hrefhttp:// vaskulitis-mainz@gmx.de/>vaskulitis-mainz@gmx.de/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon6.svg/> /div> div classcontent-block> h5>Vasculitis Stichting/h5> p>Netherlands/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://vasculitis.nl/ hrefhttps://vasculitis.nl/>www.vasculitis.nl/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon7.svg/> /div> div classcontent-block> h5>Liga Portuguesa Contra as Doencas Reumaticas/h5> p>Portugal/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.lpcdr.org.pt/ hrefhttps://www.lpcdr.org.pt/>www.lpcdr.org.pt/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon8.svg/> /div> div classcontent-block> h5>Association Vascularites/h5> p>France/Belgium/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.association-vascularites.org/ hrefhttps://www.association-vascularites.org/>www.association-vascularites.org/a> /div> /div>/div> div classd-none> div classstack-content main-block> div classcontent-block> p>Ireland/p> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2022-11/text_block_icon10.svg/> /div> div classcontent-block> h5>Asociación Española de Vasculitis Sistémicas/h5> p>Spain/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttp://www.vasculitis.es/ hrefhttp://www.vasculitis.es/>www.sid-inico.usal.es/a> /div> /div>/div> div classd-none> div classstack-content main-block> div classcontent-block> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/AMA%20logo%20%28transparent%29.png/> /div> div classcontent-block> h5>Associazione Malattie Autoimmuni/h5> p>Italy/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttp://www.associazionemalattieautoimmuni.it/ hrefhttp://www.associazionemalattieautoimmuni.it/>www.associazionemalattieautoimmuni.it/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/anmar_logo_0.png/> /div> div classcontent-block> h5>Associazione Nazionale Malati Reumatici ONLUS/h5> p>Italy/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.anmar-italia.it/ hrefhttps://www.anmar-italia.it/>www.anmar-italia.it/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/ANZ-Logo-rev.png/> /div> div classcontent-block> h5>Australia and New Zealand Vasculitis Society/h5> p>Australia / New Zealand/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.anzvasculitis.org/ hrefhttps://www.anzvasculitis.org/>www.anzvasculitis.org/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/Logo-FEDER-858x350.png/> /div> div classcontent-block> h5>Federación Española de Enfermedades Raras/h5> p>Spain/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://www.enfermedades-raras.org/ hrefhttps://www.enfermedades-raras.org/>www.enfermedades-raras.org/a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/Logo_LIRE_200_0.jpg/> /div> div classcontent-block> h5>Liga Reumatológica Española/h5> p>Spain/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://lire.es/ hrefhttps://lire.es/>lire.es//a> /div> /div>/div> div classcol-md-4> div classstack-content main-block> div classimage-block> img src/sites/multisite/understandaav/files/2023-02/pobierz-logotyp-w-formacie_0.png/> /div> div classcontent-block> h5>Vasculitis Stowarzyszenie Chorych/h5> p>Poland/p> a classcta-link target_blank data-event-categoryExternal Link Click data-event-action/home data-event-labelhttps://vasculitis.org.pl/ hrefhttps://vasculitis.org.pl/>vasculitis.org.pl//a> /div> /div>/div> /div> /div>/div> /div> /div> /div> /div> /div> /div> 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